免疫原
Synthesized peptide derived from human AGAL AA range: 138-188
特异性
This antibody detects endogenous levels of human AGAL
组成(Formulation)
Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
纯化工艺(Immunogen)
The antibody was affinity-purified from rabbit serum by affinity-chromatography using specific immunogen.
蛋白名称
Alpha-galactosidase A (EC 3.2.1.22) (Alpha-D-galactosidase A) (Alpha-D-galactoside galactohydrolase) (Melibiase) (Agalsidase)
其他名称
beta galactosidase 2;BETA GALACTOSIDASE PROTECTIVE PROTEIN;beta-galactosidase 2;beta-galactosidase protective protein;betagalactosidase 2;Carboxypeptidase C;Carboxypeptidase L;carboxypeptidase Y-like kininase;Cathepsin A;Ctsa;deamidase;EC 3.4.16.5;Glactosialidosis;GLB2;Goldberg Syndrome;GSL;lysosomal carboxypeptidase A;Lysosomal protective protein 2 kDa chain;Lysosomal protective protein;Lysosomal protective protein deficiency;NEURAMINIDASE BETA GALACTOSIDASE EXPRESSION;NGBE;Neuraminidase deficiency with beta-galactosidase deficiency;OTTHUMP31778;OTTHUMP31781;PPCA;PPCA deficiency;PPGB;PPGB_HUMAN;Protective protein cathepsin A;Protective protein for beta galactosidase;Protective protein for beta-galactosidase;Protective protein/cathepsin A deficiency;urinary kininase;AGAL;GLA;Alpha-galactosidase A (EC 3.2.1.22) (Alpha-D-galactosidase A) (Alpha-D-galactoside galactohydrolase) (Melibiase) (Agalsidase)
Fields
>>Galactose metabolism;>>Glycerolipid metabolism;>>Sphingolipid metabolism;>>Glycosphingolipid biosynthesis - globo and isoglobo series;>>Metabolic pathways;>>Lysosome